A Rare Bednar Tumour Of Neck
نویسندگان
چکیده
Pigmented dermatofibrosarcoma protuberans or previously known as Pigmented storiform neurofibroma is a rare variant of DFSP ,described by BEDNAR in 19571.The histological picture shows melanin laden dendritic cells with spindle shaped cells in storiform pattern.The tumour mostly occurs on trunk,upper and lower extremities,few in head and neck region2..It is a slow growing,locally invasive-painless cutaneous multilobulated lesion, burn or surgical scar3 at the initial stage often the cause.
منابع مشابه
Schwannoma of the Brachial Plexus: A Rare Case Report
Introduction: Brachial plexus schwannomas are extremely rare tumours of the head and neck region accounting for less than 5 % overall. Due to its rarity and anatomic complexity of the brachial plexus, schwannomas in this region present a diagnostic and surgical challenge to the surgeon. Case Report: We present a case of a 56-year-old female who presented with a slow gr...
متن کاملMesenteric Cystic Lymphangioma of Mesocolic Origin in a Three-Month-Old Infant: A Rare Differential Diagnosis of Abdominal Distension
Cystic lymphangioma is a rare benign tumour occurring during childhood. This tumour, caused by lymphatic system malformations, commonly occurs in head and neck regions. Herein, we report the case of a three-month-old male infant, diagnosed with a large cystic mass in the abdominal cavity and groin. The infant presented with low-grade fever and significant abdominal distension. Abdominal CT scan...
متن کاملReviewing the Entity: Retropharyngeal Fibrolipoma and a Rare Case Report
Introduction: Fibrolipoma, a subtype of lipoma is painless, well-circumscribed, slow-growing, submucosal benign adipocyte tumour. It is uncommon in the oral cavity and oropharyngeal region, with rare incidence in the retropharynx even rarest in pediatric age group. Case Report: A very unusual case of fibrolipoma is presented in a pediatric patient, who had a huge retropharyngeal fibrolipoma a...
متن کاملRhabdomyosarcoma: Nose Presenting As Second Primary with Carcinoma Tongue
Introduction Presence of two primary malignancies is rare and occurs in 3-5% of the cancer patients. As per our extensive internet research, this is the only reported case of a synchronous sino-nasal embryonal rhabdomyosarcoma with squamous cell carcinoma-tongue. The case report is important because of the rare diagnosis and the challenge we faced in the diagnosis and treatment of the pat...
متن کاملSuccessful treatment of pigmented dermatofibrosarcoma protuberance on the nasal root with cyberknife radiosurgery.
© 2012 The Authors. doi: 10.2340/00015555-1357 Journal Compilation © 2012 Acta Dermato-Venereologica. ISSN 0001-5555 Dermatofibrosarcoma protuberans (DFSP) is a fibrohistiocytic tumour of intermediate malignancy characterized by slow infiltrative growth and a high tendency to recur locally. Pigmented DFSP, also known as Bednar tumour, is a rare variant of DFSP and accounts for up to 5% of all D...
متن کامل